EVALUATION OF HEART INVOLVEMENT IN CALPAINOPATHY (LGMD2A) USING CARDIOVASCULAR MAGNETIC RESONANCE

SILVIO QUICK, MD, JOCHEN SCHAEFER, MD, NADINE WAESSNIG, MD,
THORSTEN SCHULTHEISS, MD, ULRIKE REUNER, MD, STEFFEN SCHOEN, MD,
HEINZ REICHMANN, MD, RUTH STRASSER, MD, PhD, and UWE SPEISER, MD


Cardiac dysfunction occurs in several forms of limb girdle muscular dystrophy (LGMD). The aim of this study was to investigate cardiac involvement in calpainop- athy (LGMD2A). Methods: Cardiovascular evaluation was per- formed in 10 patients with genetically verified LGMD2A by